Carcinoma of esophagus, salivary gland type

Orpha code: 418945OMIM code:

Definition

A rare gastroesophageal tumor characterized by a typically submucosal tumor occurring usually in the middle to distal esophagus and histologically characterized as either mucoepidermoid (intimate mixture of mucus, intermediate, and epidermoid cells) or as adenoid cystic carcinoma (biphasic admixture of duct‐lining epithelial and myoepithelial cells with tubular, cribriform, solid, or basaloid growth patterns). Patients may be asymptomatic or may present with progressive dysphagia, heartburn, retrosternal pain and/or weight loss.

Disease data
Classification

Disease

Synonyms
Esophageal carcinoma, salivary gland type
Esophageal carcinoma, salivary gland type
ORPHA code
418945
OMIM code
-
ICD10 code
C15.0
ICD11 code
-

No additional description.

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