Primary failure of tooth eruption

Orpha code: 412206OMIM code: 125350

Definition

A rare genetic odontologic disease characterized by failure of eruption of non-ankylosed permanent teeth without evidence of obvious mechanical obstruction. Posterior teeth are preferentially affected (typically with involvement of all teeth distal to the most mesial non-erupted tooth), resulting in a posterior open bite. Non-ankylosed teeth tend to become ankylosed, and orthodontic treatment of affected teeth is generally unsuccessful.

Disease data
Classification

Disease

Synonyms
PFE
PFE
Pierwotne zatrzymanie zębów
Primary retention of teeth
ORPHA code
412206
OMIM code
125350
ICD10 code
K00.8
ICD11 code
-

No additional description.

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