Generalized eruptive keratoacanthoma

Orpha code: 411777OMIM code:

Definition

Generalized eruptive keratoacanthoma (GEKA) is rare variant of keratoacanthoma (KA) that affects the skin and mucous membranes and which is characterized by a sudden generalized eruption of severely pruritic, hundreds to thousands of small follicular papules, often with a central keratotic plug.

Disease data
Classification

Disease

Synonyms
GEKA
GEKA
Uogólniony rozsiany rogowiak kolczystokomórkowy Grzybowskiego
Zespół Grzybowskiego
Generalized eruptive keratoacanthomas of Grzybowski
Grzybowski syndrome
ORPHA code
411777
OMIM code
-
ICD10 code
L85.8
ICD11 code
-

No additional description.

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