Mild phosphoribosylpyrophosphate synthetase superactivity

Orpha code: 411536OMIM code: 300661

Definition

A mild form of phosphoribosylpyrophosphate (PRPP) synthetase superactivity, an X-linked disorder of purine metabolism, characterized by adolescent or early adult-onset hyperuricemia and hyperuricosuria, leading to urolithiasis and gout.

Disease data
Classification

Clinical subtype

Synonyms
Mild PRPP synthetase superactivity
Łagodna nadczynność PRPS1
Łagodna nadczynność syntetazy PRPP
Mild PRPS1 superactivity
ORPHA code
411536
OMIM code
300661
ICD10 code
E79.8
ICD11 code
-

No additional description.

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