Clear cell adenocarcinoma of the ovary

Orpha code: 398971OMIM code:

Definition

A rare, malignant, epithelilal ovarian neoplasm, composed of clear, eosinophilic and hobnail cells displaying variable degrees of tubulocystic, papillary and solid histological patterns, macroscopically appearing as a typically unilateral mass in the ovary which ranges from solid to cystic. Patients are often diagnosed in early stages and usually present with pelvic pain and pressure, an abdominal mass and/or gastrointestinal problems, such as early satiety or bloating. Association with Lynch syndrome has been reported.

Disease data
Classification

Disease

Synonyms
Ovarian clear cell adenocarcinoma
Gruczolakorakowiak jasnokomórkowy jajnika
ORPHA code
398971
OMIM code
-
ICD10 code
C56
ICD11 code
-

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl