Neonatal scleroderma

Orpha code: 398127OMIM code:

Definition

Neonatal scleroderma is a very rare, secondary, neonatal autoimmune disease characterized by neonatal-onset of erythematous skin lesions with a linear appearance that gradually become indurated and hyperpigmented and progressively present skin atrophy. Positive serum antibodies (in particular antinuclear antibodies and/or rheumatoid factor) may be associated.

Disease data
Classification

Disease

ORPHA code
398127
OMIM code
-
ICD10 code
P83.8
ICD11 code
-

No additional description.

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