Neonatal dermatomyositis

Orpha code: 398117OMIM code:

Definition

Neonatal dermatomyositis is a very rare, secondary, neonatal autoimmune disease characterized by generalized weakness, severe hypotonia, absent or reduced deep tendon reflexes, and highly elevated serum creatine kinase levels presenting in the neonatal period. Perifascicular atrophy in the presence of a diffuse perivascular inflammatory cell exudate is observed on muscle biopsy.

Disease data
Classification

Disease

Synonyms
Neonatal DM
DM noworodków
ORPHA code
398117
OMIM code
-
ICD10 code
M33.1
ICD11 code
-

No additional description.

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