Peripheral neuropathy-myopathy-hoarseness-hearing loss syndrome

Orpha code: 397744OMIM code: 614369

Definition

Peripheral neuropathy-myopathy-hoarseness-hearing loss syndrome is a rare, syndromic genetic deafness characterized by a combination of muscle weakness, chronic neuropathic and myopathic features, hoarseness and sensorineural hearing loss. A wide range of disease onset and severity has been reported even within the same family.

Disease data
Classification

Disease

Synonyms
Peripheral neuropathy-myopathy-hoarseness-deafness syndrome
Zespół neuropatia obwodowa-miopatia-chrypka-głuchota
ORPHA code
397744
OMIM code
614369
ICD10 code
G60.0
ICD11 code
-

No additional description.

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