Fatal post-viral neurodegenerative disorder

Orpha code: 391343OMIM code:

Definition

Fatal post-viral neurodegenerative disorder is a rare neuroinflammatory disease characterized by the onset of ataxia, dysarthia and cerebral white matter changes which are triggered by viral infection. Episodic progressive neurodegeneration (manifesting with loss of motor and verbal skills, muscle weakness, further cerebral white matter degeneration and, eventually, death) is observed in the absence of hematopathology, cytokine overproduction, fever, hypertrigliceridemia, hypofibrinogenemia and hyperferritinemia.

Disease data
Classification

Disease

ORPHA code
391343
OMIM code
-
ICD10 code
G04.8
ICD11 code
-

No additional description.

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