Susceptibility to viral and mycobacterial infections due to STAT1 deficiency

Orpha code: 391311OMIM code: 613796

Definition

A rare, genetic, primary immunodeficiency due to a defect in innate immunity disorder characterized by impaired intracellular signaling from both type I and type II interferons, leading to early-onset, severe, life-threatening intracellular bacterial (typically mycobacteria) and viral (mainly herpes viruses) infections.

Disease data
Classification

Disease

Synonyms
Predisposition to severe viral infection due to STAT1 deficiency
STAT1 deficiency
Predisposition to severe viral infection due to STAT1 deficiency
STAT1 deficiency
ORPHA code
391311
OMIM code
613796
ICD10 code
D84.8
ICD11 code
-

No additional description.

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