Guanidinoacetate methyltransferase deficiency

Orpha code: 382OMIM code: 612736

Definition

Guanidinoacetate methyltransferase (GAMT) deficiency is a creatine deficiency syndrome characterized by global developmental delay/intellectual disability (DD/ID), prominent speech delay, autistic/hyperactive behavioral disorders, seizures, and various types of pyramidal and/or extra-pyramidal manifestations.

Disease data
Classification

Disease

Synonyms
GAMT deficiency
Niedobór GAMT
ORPHA code
382
OMIM code
612736
ICD10 code
E72.8
ICD11 code
5C53.4

No additional description.

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