Description of the disease * EnglishPolish Pobierz sekcję do PDF Definicja A rare, aggressive, malignant, neoplastic disease characterized by a usually ill-defined, solid, multilobulated mass, frequently having necrosis, located on any site of the body (except the central nervous system), composed of small, round, poorly differentiated cells, with or without Homer-Wright rosettes, showing varying degrees of neuroectodermal differentiation. Manifestations are variable depending on location, with osteolytic destruction being common when arising from bone. Disease data Klasyfikacja Disease Synonimy PPNET Obwodowy PNET PPNET Peripheral PNET Peripheral neuroepithelioma Kod ORPHA 370348 Kod OMIM 612219 Kod ICD10 C71.9 Kod ICD11 XH6P76 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl