White platelet syndrome

Definition

White platelet syndrome (WPS) is is a platelet granule disorder characterized by thrombocytopenia, increased mean platelet volumes, decreased platelet responsiveness to aggregating agents, and significant defects in platelet ultrastructural morphology leading to prolonged bleeding times and bleeding.

Disease data

Classification

Disease

ORPHA code

370131

OMIM code

ICD10 code

D69.1

ICD11 code

*Soruce