2p21 microdeletion syndrome without cystinuria

Orpha code: 369881OMIM code:

Definition

2p21 microdeletion syndrome without cystinuria is a rare partial autosomal monosomy characterized by weak fetal movements, severe infantile hypotonia and feeding difficulties that spontaneously improve with time, urogenital abnormalities (hypospadias or hypoplastic labia majora), global development delay, mild intellectual disability and facial dysmorphism (dolichocephaly, frontal bossing, bilateral ptosis, midface retrusion, open mouth with tented upper lip vermilion). Affected individuals have borderline elevated serum lactate but no cystinuria.

Disease data
Classification

Malformation syndrome

Synonyms
Del(2)(p21) without cystinuria
Del(2)(p21) bez cystynurii
ORPHA code
369881
OMIM code
-
ICD10 code
Q93.5
ICD11 code
-

No additional description.

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