Intellectual disability-hyperkinetic movement-truncal ataxia syndrome

Orpha code: 369847OMIM code:

Definition

A rare, genetic, syndromic intellectual disability disease characterized by global developmental delay, microcephaly, mild to moderate intellectual disability, truncal ataxia, trunk and limb, or generalized, choreiform movements, and elevated serum creatine kinase levels. Variably associated features include mild cerebral atrophy, muscular weakness or hypotonia in early childhood, and/or seizures. Ocular abnormalities (e.g. exophoria, anisometropia, amblyopia) have been reported.

Disease data
Classification

Disease

ORPHA code
369847
OMIM code
-
ICD10 code
G25.5
ICD11 code
-

No additional description.

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