Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition Severe early childhood onset retinal dystrophy (SECORD) is an inherited retinal dystrophy characterized by a severe congenital night blindness, progressive retinal dystrophy and nystagmus. Best corrected visual acuity can reach 0.3 in the first decade of life and can pertain well into the second decade of life. Blindness is often complete by the age of 30 years. Disease data Classification Disease Synonyms EOSRD Ciężka dystrofia siatkówki o wczesnym początku EOSRD SECORD Early-onset severe retinal dystrophy SECORD ORPHA code 364055 OMIM code - ICD10 code H35.5 ICD11 code - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl