Description of the disease * EnglishPolish Pobierz sekcję do PDF Definicja A very rare Epstein-Barr virus-associated lymphoproliferative disorder characterized by a chronic, recurrent, vesiculopapular rash, which subsequently ulcerates and scars, located mainly on sun-exposed areas and which is associated with systemic manifestations, such as fever, weight loss, asthenia, facial edema, arthralgia, lymphadenopathy, hepatosplenomegaly and/or increased liver enzymes. Hypersensitivity to mosquito bites has been associated and an increased risk of developing systemic lymphoma has been reported. Disease data Klasyfikacja Disease Synonimy Angiocentric cutaneous T-cell lymphoma of childhood HVLL HVLL Hydroa-like cutaneous T-cell lymphoma Kod ORPHA 364039 Kod OMIM - Kod ICD10 C84.5 Kod ICD11 - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl