Hydroa vacciniforme-like lymphoma

Orpha code: 364039OMIM code:

Definicja

A very rare Epstein-Barr virus-associated lymphoproliferative disorder characterized by a chronic, recurrent, vesiculopapular rash, which subsequently ulcerates and scars, located mainly on sun-exposed areas and which is associated with systemic manifestations, such as fever, weight loss, asthenia, facial edema, arthralgia, lymphadenopathy, hepatosplenomegaly and/or increased liver enzymes. Hypersensitivity to mosquito bites has been associated and an increased risk of developing systemic lymphoma has been reported.

Disease data
Klasyfikacja

Disease

Synonimy
Angiocentric cutaneous T-cell lymphoma of childhood
HVLL
HVLL
Hydroa-like cutaneous T-cell lymphoma
Kod ORPHA
364039
Kod OMIM
-
Kod ICD10
C84.5
Kod ICD11
-

No additional description.

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