Childhood-onset autosomal recessive myopathy with external ophthalmoplegia

Orpha code: 363677OMIM code: 605637

Definicja

A rare, genetic, non-dystrophic myopathy disease characterized by childhood-onset severe external ophthalmoplegia, typically without ptosis, associated with mild, very slowly progressive muscular weakness and atrophy, involving the facial, neck flexor and limb (upper > lower, proximal > distal) muscles. Muscle biopsy shows type 1 fiber uniformity, absent, or abnormally small, type 2A fibers, increased variability of fiber size, internalized nuclei and/or fatty infiltration.

Disease data
Klasyfikacja

Disease

Kod ORPHA
363677
Kod OMIM
605637
Kod ICD10
G71.2
Kod ICD11
-

No additional description.

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