New-onset refractory status epilepticus

Orpha code: 363558OMIM code:

Definition

New-onset refractory status epilepticus is an acute encephalopathy with inflammation-mediated status epilepticus characterized by an acute refractory status epilepticus, typically of the tonic-clonic type, following prodromal symptoms of confusion, fever, fatigue, headache, symptoms of gastrointestinal or upper respiratory tract infection, behavioral changes or hallucinations. Brain MRI abnormalities and abnormal findings in CSF, including pleocytosis and/or elevated protein levels, are frequently found during acute episode. Treatment-resistant epilepsy, cognitive and psychiatric impairments are usual consequences.

Disease data
Classification

Disease

Synonyms
NORSE
NORSE
ORPHA code
363558
OMIM code
-
ICD10 code
G41.8
ICD11 code
-

No additional description.

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