Malignant sex cord stromal tumor of ovary

Orpha code: 35808OMIM code:

Definition

Malignant sex cord stromal tumor (SCST) of ovary is a rare ovarian cancer (see this term) arising from granulosa, theca, sertoli and leydig cells or stromal fibroblasts, occurring at any age and presenting with abdominal or pelvic mass, and characterized (with the exception of fibroma) by the production of sex steroids resulting in manifestations of hormone excess, with a relatively favorable prognosis.

Disease data
Classification

Category

Synonyms
Malignant ovarian SCST
Złośliwy SCST jajnika
Malignant ovarian sex cord-stromal tumor
ORPHA code
35808
OMIM code
-
ICD10 code
C56
ICD11 code
-

No additional description.

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