Truncus arteriosus

Orpha code: 3384OMIM code: 217095

Definition

Truncus arteriosus (TA) is a rare congenital cardiovascular anomaly characterized by a single arterial trunk arising from the heart by means of a single semilunar valve (<I>i.e.</I> truncal valve). Pulmonary arteries originate from the common arterial trunk distal to the coronary arteries and proximal to the first brachiocephalic branch of the aortic arch. TA typically overrides a large outlet ventricular septal defect (VSD). The intracardiac anatomy usually displays situs solitus and atrioventricular (AV) concordance.

Disease data
Classification

Morphological anomaly

Synonyms
Common aorticopulmonary trunk
TAC
Wspólny pień tętniczo-płucny
Common arterial trunk
TAC
ORPHA code
3384
OMIM code
217095
ICD10 code
Q20.0
ICD11 code
LA85.4

No additional description.

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