Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A rare congenital respiratory disorder characterized by marked dilatation of the trachea and proximal bronchi that leads to impaired airway secretion clearance and recurrent lower respiratory tract infections. Disease data Classification Clinical syndrome Synonyms Congenital tracheobronchomegaly Tracheobronchomegalia Tracheobronchomegalia idiopatyczna Tracheobronchomegalia wrodzona Idiopathic tracheobronchomegaly Tracheobronchomegaly ORPHA code 3347 OMIM code 275300 ICD10 code J98.0 ICD11 code CA27.1 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl