Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A very rare genetic necrotic bone disorder characterized clinically by painless swelling of the proximal interphalangeal joints associated with osteonecrosis of epiphyses followed by osteoarthritic changes, with onset before 25 years of age and often a benign course. Disease data Classification Disease Synonyms Aseptic necrosis of phalangeal epiphyses Aseptyczna martwica nasad paliczków Zapalenie kości i chrząstek nasad paliczków Osteochondrosis of phalangeal epiphyses ORPHA code 3314 OMIM code 165700 ICD10 code M93.2 ICD11 code FB82.1 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl