Actinic prurigo

Orpha code: 330061OMIM code: 174770

Definition

A rare, chronic, photodermatosis disease characterized by intensely pruritic, polymorphic, erythematous, excoriated and/or lichenified papules, macules, plaques and nodules, occurring on sun-exposed areas of the skin (particularly face, nose, lips, and ears), frequently associating cheilitis (especially of the lower lip) and conjuctivitis, which are present year-round or only in the spring/summer (depending on geographic location), observed mainly in Native Americans and Mestizos. Cheilitis may be the sole clinical presentation. Histologically, the presence of lymphoid follicles in mucosa is pathognomonic.

Disease data
Classification

Disease

Synonyms
Familial polymorphous light eruption of American Indians
Dziedziczne wielopostaciowe osutki świetlne amerykańskich Indian
Rodzinne wielopostaciowe osutki świetlne amerykańskich Indian
Świerzbiączka letnia
Świerzbiączka letnia Hutchinsona
Świerzbiączka letnia guzkowa
Wielopostaciowe osutki świetlne
Hereditary polymorphous light eruption of American Indians
Hutchinson summer prurigo
Hydroa aestivale
ORPHA code
330061
OMIM code
174770
ICD10 code
L56.4
ICD11 code
EJ30.Y

No additional description.

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