Hydroa vacciniforme

Orpha code: 330058OMIM code:

Definition

A rare photodermatosis characterized by the development of pruritic or painful vesicles in a photodistributed pattern in response to sunlight exposure. The lesions heal with permanent varioliform scarring. Ocular involvement, deformities of ears and nose, or contractures of the fingers may occasionally be observed. Systemic signs and symptoms are absent. The condition typically occurs in childhood and regresses spontaneously in adolescence or young adulthood.

Disease data
Classification

Disease

ORPHA code
330058
OMIM code
-
ICD10 code
L56.4
ICD11 code
EJ30.Y

No additional description.

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