C3 glomerulopathy

Orpha code: 329918OMIM code: 614809

Definition

A form of primary membranoproliferative glomerulonephritis characterized by the presence in renal biopsy samples of a glomerulonephritis with sole (or at least dominant) glomerular immunofluorescence staining for C3. Non-specific alterations or proliferative patterns with C3-dominant glomerular staining are also possible. Based upon electron microscopic findings, C3 glomerulopathy (C3G) may be further classified as C3 glomerulonephritis (C3GN) or Dense deposit disease (DDD).

Disease data
Classification

Clinical subtype

Synonyms
Non-Ig-mediated MPGN
Błoniasto-rozplemowe kłębuszkowe zapalenie nerek nie wywoływane przez Ig
Glomerulopatia C3
MPGN nie związane z Ig
MPGN nie związane z przeciwciałami MPGN
Non-Ig-mediated membranoproliferative glomerulonephritis
Non-immunoglobulin-mediated MPGN
Non-immunoglobulin-mediated membranoproliferative glomerulonephritis
ORPHA code
329918
OMIM code
614809
ICD10 code
N03.5
ICD11 code
-

No additional description.

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