Idiopathic giant cell myocarditis

Orpha code: 329874OMIM code:

Definition

A rare cardiomyopathy characterized by progressive myocarditis with diffuse infiltration of cardiac tissue by lymphocytes, macrophages, multinuclear giant cells, and myocardial necrosis. Clinical presentation includes rapidly progressive heart failure, ventricular arrhythmias, complete heart block, and sudden cardiac death. Some patients have associated autoimmune disorders.

Disease data
Classification

Disease

Synonyms
IGCM
IGCM
ORPHA code
329874
OMIM code
-
ICD10 code
I40.1
ICD11 code
-

No additional description.

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