Lipoprotein glomerulopathy

Orpha code: 329481OMIM code: 611771

Definition

A rare genetic renal disease characterized by the formation of intraglomerular lipoprotein thrombi due to lipid deposition in severely dilated glomerular capillaries. Laboratory examination reveals abnormal serum lipid profiles, in particular markedly elevated apolipoprotein E. Clinical manifestations include proteinuria or nephrotic syndrome with hypertension and potential progression to chronic renal failure. Systemic complications of dyslipidemia are not observed.

Disease data
Classification

Disease

Synonyms
LPG
LPG
ORPHA code
329481
OMIM code
611771
ICD10 code
N07.8
ICD11 code
-

No additional description.

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