Cenani-Lenz syndrome

Orpha code: 3258OMIM code: 212780

Definition

Cenani-Lenz syndrome (CLS) is a congenital malformation syndrome that associates a complex syndactyly of the hands with malformations of the forearm bones and similar manifestations in the lower limbs.

Disease data
Classification

Malformation syndrome

Synonyms
Cenani syndactyly
Syndaktylia Cenani
Syndaktylia Cenani i Lenza
Syndaktylia typu 7
Cenani-Lenz syndactyly
Syndactyly type 7
ORPHA code
3258
OMIM code
212780
ICD10 code
Q78.4
ICD11 code
LB79.Y

No additional description.

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