Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition Stapes fixation (stapedovestibular ankylosis) is a hearing loss condition that appears as a consequence of annular ligament destruction followed by excessive connective tissue production during the healing process. This condition is mainly observed in otosclerosis, but is also found in chronic otitis media with tympanosclerosis, and other rare bone diseases such as Paget's disease and osteogenesis imperfecta (Lobstein disease). Disease data Classification Malformation syndrome Synonyms Progressive hearing loss with stapes fixation Ankyloza strzemiączkowo-przedsionkowa Zespół Thiesa i Reisa Stapedo-vestibular ankylosis Thies-Reis syndrome ORPHA code 3235 OMIM code 601449 ICD10 code H74.3 ICD11 code LD2H.2 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl