Multilocular cystic renal neoplasm of low malignant potential

Orpha code: 319287OMIM code:

Definicja

Multilocular cystic renal neoplasm of low malignant potential is a rare subtype of clear cell renal cell carcinoma with distinct pathological features of cysts lined by occasionally flattened cuboidal clear cells and septa containing aggregates of epithelial cells with clear cytoplasm, and excellent prognosis. The tumor usually presents as an asymptomatic, unilateral, solitary lesion, macroscopically consisting of numerous, fluid-filled, septated cysts of variable size. Rarely, the symptoms typically associated with renal tumors (flank pain, hematuria, palpable mass) may be present.

Disease data
Klasyfikacja

Histopathological subtype

Synonimy
MCRCC
MCRCC
Wieloogniskowy torbielowaty rak z komórek nerkowych
Wieloogniskowy torbielowaty gruczolakorak z komórek nerkowych
Multilocular clear cell adenocarcinoma
Multilocular clear cell carcinoma
Multilocular clear cell renal cell adenocarcinoma
Multilocular clear cell renal cell carcinoma
Multilocular cystic renal cell adenocarcinoma
Multilocular cystic renal cell carcinoma
Kod ORPHA
319287
Kod OMIM
-
Kod ICD10
C64
Kod ICD11
-

No additional description.

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