Multilocular cystic renal neoplasm of low malignant potential

Orpha code: 319287OMIM code:

Definition

Multilocular cystic renal neoplasm of low malignant potential is a rare subtype of clear cell renal cell carcinoma with distinct pathological features of cysts lined by occasionally flattened cuboidal clear cells and septa containing aggregates of epithelial cells with clear cytoplasm, and excellent prognosis. The tumor usually presents as an asymptomatic, unilateral, solitary lesion, macroscopically consisting of numerous, fluid-filled, septated cysts of variable size. Rarely, the symptoms typically associated with renal tumors (flank pain, hematuria, palpable mass) may be present.

Disease data
Classification

Histopathological subtype

Synonyms
MCRCC
MCRCC
Wieloogniskowy torbielowaty rak z komórek nerkowych
Wieloogniskowy torbielowaty gruczolakorak z komórek nerkowych
Multilocular clear cell adenocarcinoma
Multilocular clear cell carcinoma
Multilocular clear cell renal cell adenocarcinoma
Multilocular clear cell renal cell carcinoma
Multilocular cystic renal cell adenocarcinoma
Multilocular cystic renal cell carcinoma
ORPHA code
319287
OMIM code
-
ICD10 code
C64
ICD11 code
-

No additional description.

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