Eosinophilic fasciitis

Orpha code: 3165OMIM code: 226350

Definicja

A rare idiopathic inflammatory myopathy that is characterized by inflammation and thickening of the fascia, usually associated with peripheral eosinophilia. It presents during adulthood with symmetrical and painful swelling of mainly the extremities that progressively become indurated. Fatigue, disabling cutaneous fibrosis, myositis and arthritis may also be observed.

Disease data
Klasyfikacja

Disease

Synonimy
Diffuse fasciitis with eosinophilia
Rozlane zapalenie powięzi z eozynofilią
Zespół Shulmana
Shulman syndrome
Kod ORPHA
3165
Kod OMIM
226350
Kod ICD10
M35.4
Kod ICD11
4A43.4

No additional description.

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