Eosinophilic fasciitis

Orpha code: 3165OMIM code: 226350

Definition

A rare idiopathic inflammatory myopathy that is characterized by inflammation and thickening of the fascia, usually associated with peripheral eosinophilia. It presents during adulthood with symmetrical and painful swelling of mainly the extremities that progressively become indurated. Fatigue, disabling cutaneous fibrosis, myositis and arthritis may also be observed.

Disease data
Classification

Disease

Synonyms
Diffuse fasciitis with eosinophilia
Rozlane zapalenie powięzi z eozynofilią
Zespół Shulmana
Shulman syndrome
ORPHA code
3165
OMIM code
226350
ICD10 code
M35.4
ICD11 code
4A43.4

No additional description.

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