Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A rare idiopathic inflammatory myopathy that is characterized by inflammation and thickening of the fascia, usually associated with peripheral eosinophilia. It presents during adulthood with symmetrical and painful swelling of mainly the extremities that progressively become indurated. Fatigue, disabling cutaneous fibrosis, myositis and arthritis may also be observed. Disease data Classification Disease Synonyms Diffuse fasciitis with eosinophilia Rozlane zapalenie powięzi z eozynofilią Zespół Shulmana Shulman syndrome ORPHA code 3165 OMIM code 226350 ICD10 code M35.4 ICD11 code 4A43.4 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl