Ovarian fibrothecoma

Orpha code: 314478OMIM code:

Definition

Ovarian fibrothecoma is a rare, benign, sex cord-stromal neoplasm, with a typically unilateral location in the ovary, characterized by mixed features of both fibroma and thecoma. Patients may be asymptomatic or may present with pelvic/abdominal pain and/or distension and, occasionally, with post-menopausal bleeding. Large tumors (>10cm) are often associated with pleural effusion and ascites (the Meigs syndrome triad).

Disease data
Classification

Disease

ORPHA code
314478
OMIM code
-
ICD10 code
D27
ICD11 code
-

No additional description.

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