Coats plus syndrome

Orpha code: 313838OMIM code: 612199

Definition

Coats plus syndrome is a pleiotropic multisystem disorder characterized by retinal telangiectasia and exudates, intracranial calcification with leukoencephalopathy and brain cysts, osteopenia with predisposition to fractures, bone marrow suppression, gastrointestinal bleeding and portal hypertension. It is transmitted as an autosomal recessive disease.

Disease data
Classification

Disease

Synonyms
CRMCC
CRMCC
Mikroangiopatia mózgowo-siatkówkowa ze zwapnieniami i torbielami
Cerebroretinal microangiopathy with calcifications and cysts
ORPHA code
313838
OMIM code
612199
ICD10 code
H35.0
ICD11 code
-

No additional description.

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