Description of the disease * EnglishPolish Pobierz sekcję do PDF Definicja A rare acquired immunodeficiency disorder characterized by the appearance of susceptibility to disseminated opportunistic infections (in particular, disseminated nontuberculous mycobacterial infection, salmonellosis, penicillosis, and varicella zoster virus infection) in previously healthy (HIV-negative) adults, associated with the presence of acquired autoantibodies to interferon gamma. Typical clinical manifestation includes lymphadenopathy (cervical or generalized), fever, weight loss and/or reactive skin lesions. Disease data Klasyfikacja Disease Synonimy Acquired adult-onset immunodeficiency Niedobór odporności o początku w wieku dorosłym z autoprzeciwciałami anty interferon gamma Adult-onset immunodeficiency with acquired anti-interferon-gamma autoantibodies Kod ORPHA 306431 Kod OMIM - Kod ICD10 D84.8 Kod ICD11 - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl