Primary cutaneous anaplastic large cell lymphoma

Orpha code: 300865OMIM code:

Definition

Primary cutaneous anaplastic large cell lymphoma (C-ALCL) is a rare T-cell non-Hodgkin lymphoma that affects the skin and generally shows no extracutaneous involvement at presentation. It belongs to the spectrum of primary cutaneous CD30+ lymphoproliferative disorders along with lymphomatoid papulosis (see this term) with which it shares overlapping clinical and histopathologic features.

Disease data
Classification

Disease

Synonyms
Primary C-ALCL
Histiocytoza regresywna atypowa
Primary C-ALCL
Regressive atypical histiocytosis
ORPHA code
300865
OMIM code
-
ICD10 code
C86.6
ICD11 code
2B03.0

No additional description.

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