T-cell/histiocyte rich large B cell lymphoma

Orpha code: 300857OMIM code:

Definition

T-cell/histiocyte rich large B cell lymphoma (THRLBCL) is a rare variant of diffuse large B-cell lymphoma (DLBCL; see this term), mainly affecting middle-aged men and often not being discovered until an advanced disease stage, with involvement of the spleen, liver and bone marrow occurring at a greater frequency than in DLBCL. It is often difficult to diagnose due to its similarity with other lymphoid diseases such as classic Hodgkin lymphoma and nodular lymphocyte-predominant Hodgkin lymphoma (see these terms) and has an aggressive clinical course.

Disease data
Classification

Disease

Synonyms
THRLBCL
THRLBCL
ORPHA code
300857
OMIM code
-
ICD10 code
C83.3
ICD11 code
2A81.4

No additional description.

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