Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition Oligodontia-cancer predisposition syndrome is a rare, genetic, odontologic disease characterized by congenital absence of six or more permanent teeth (excluding the third molars) in association with an increased risk for malignancies, ranging from gastrointestinal polyposis to early-onset colorectal cancer and/or breast cancer. Ectodermal dysplasia (manifesting with sparse hair and/or eyebrows) may also be associated. Disease data Classification Disease Synonyms Autosomal dominant ectodermal dysplasia-cancer predisposition syndrome Zespół autosomalna dominująca dysplazja ektodermalna - predyspozycja do nowotworów ORPHA code 300576 OMIM code 608615 ICD10 code C19 ICD11 code - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl