Celiac artery compression syndrome

Orpha code: 293208OMIM code:

Definition

A rare disease caused by compression of the celiac axis by an abnormally shaped arcuate ligament (the part of the diaphragm in which both pillars join in the midline around the aorta). Patients have recurrent abdominal pain, anorexia and weight loss. The pain is epigastric, and diarrhea or constipation may be present as well. Onset of pain will usually, although not always, be after food intake, and may be associated with nausea and emesis. Other symptoms may include lassitude, exercise intolerance and vomiting. Occasionally, a patient may show an abdominal murmur upon auscultation.

Disease data
Classification

Disease

Synonyms
Dunbar syndrome
MALS
Median arcuate ligament syndrome
Dunbar syndrome
MALS
Median arcuate ligament syndrome
ORPHA code
293208
OMIM code
-
ICD10 code
I77.4
ICD11 code
BD52.5

No additional description.

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