Hereditary acrokeratotic poikiloderma

Orpha code: 2907OMIM code:

Definition

A rare hereditary poikiloderma characterized by infantile onset of vesicopustule formation on hands and feet and widespread eczematoid dermatitis (both spontaneously resolving during childhood), as well as gradually developing diffuse poikiloderma with striate and reticulate atrophy (excluding the face, scalp, and ears), and development of keratotic papules on hands, feet, elbows, and knees, beginning in early childhood. There have been no further descriptions in the literature since 1981.

Disease data
Classification

Disease

Synonyms
Weary syndrome
Wrodzona poikilodermia z pęcherzami, typu Weary
ORPHA code
2907
OMIM code
-
ICD10 code
Q82.8
ICD11 code
LD2B

No additional description.

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