Idiopathic chronic eosinophilic pneumonia

Orpha code: 2902OMIM code:

Definition

A rare, severe, interstitial lung disease characterized by insidious onset with subacute or chronic non-specific respiratory manifestations (dyspnea, cough, wheezing) often associated with systemic manifestations (fatigue, malaise, weight loss) and a history of asthma (up to half of patients). Eosinophilia is present in most cases, usually in excess of 1000 cells/mm3.

Disease data
Classification

Disease

Synonyms
Chronic eosinophilic pneumonia
Przewlekłe eozynofilowe zapalenie płuc
ORPHA code
2902
OMIM code
-
ICD10 code
J82
ICD11 code
CB02.11

No additional description.

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