Vitamin B12-unresponsive methylmalonic acidemia type mut0

Orpha code: 289916OMIM code: 251000

Definition

Vitamin B12-unresponsive methylmalonic acidemia type mut0 is an inborn error of metabolism characterized by recurrent ketoacidotic comas or transient vomiting, dehydration, hypotonia and intellectual deficit, which does not respond to administration of vitamin B12.

Disease data
Classification

Clinical subtype

Synonyms
Complete deficiency of methylmalonyl-CoA mutase
Acyduria metylomalonowa typu mut0 niewrażliwa na witaminę B12
Całkowity Niedobór mutazy metylomalonylo-CoA
Vitamin B12-unresponsive methylmalonic aciduria type mut0
ORPHA code
289916
OMIM code
251000
ICD10 code
E71.1
ICD11 code
-

No additional description.

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