Pityriasis rubra pilaris

Orpha code: 2897OMIM code: 173200

Definition

Pityriasis rubra pilaris is a rare chronic papulosquamous disorder of unknown etiology characterized by small follicular papules, scaly red-orange patches, and palmoplantar hyperkeratosis, which may progress to plaques or erythroderma. Although most of the cases are sporadic and acquired, a familial form of the disease exists.

Disease data
Classification

Disease

ORPHA code
2897
OMIM code
173200
ICD10 code
L44.0
ICD11 code
EA94

No additional description.

Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl