Pityriasis rubra pilaris

Orpha code: 2897OMIM code: 173200

Definicja

Pityriasis rubra pilaris is a rare chronic papulosquamous disorder of unknown etiology characterized by small follicular papules, scaly red-orange patches, and palmoplantar hyperkeratosis, which may progress to plaques or erythroderma. Although most of the cases are sporadic and acquired, a familial form of the disease exists.

Disease data
Klasyfikacja

Disease

Kod ORPHA
2897
Kod OMIM
173200
Kod ICD10
L44.0
Kod ICD11
EA94

No additional description.

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