Phakomatosis pigmentokeratotica

Orpha code: 2874OMIM code:

Definition

A rare epidermal nevus disorder characterized by the association of speckled lentiginous nevi with epidermal sebaceous nevi, and extracutaneous anomalies.

Disease data
Classification

Malformation syndrome

ORPHA code
2874
OMIM code
-
ICD10 code
Q85.8
ICD11 code
LD2D.Y

No additional description.

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