Infantile-onset autosomal recessive nonprogressive cerebellar ataxia

Orpha code: 284332OMIM code: 608029

Definicja

A rare, genetic, autosomal recessive cerebellar ataxia disease characterized by nonprogressive cerebellar ataxia, with onset in infancy, manifesting with delayed motor and speech development, gait ataxia, dysmetria, hypotonia, increased deep tendon reflexes, and dysarthria. Additional variable manifestations include moderate nystagmus on lateral gaze, mild spasticity, intention tremor, short stature and pes planus. Brain imaging reveals cerebellar vermis atrophy.

Disease data
Klasyfikacja

Disease

Synonimy
Autosomal recessive spinocerebellar ataxia type 6
Autosomalna recesywna ataksja rdzeniowo-móżdżkowa-6
SCAR6
SCAR6
Kod ORPHA
284332
Kod OMIM
608029
Kod ICD10
G11.0
Kod ICD11
-

No additional description.

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