Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A rare subtype of congenital pulmonary airway malformation characterized by a multicystic mass of non-functioning lung tissue consisting of numerous microcysts of less than 0.5 cm in diameter. The lesions have intracystic communications, can be connected to the tracheobronchial tree, and are usually unilateral, involving an entire lobe. The condition may be associated with polyhydramnios, fetal hydrops, and stillbirth, or present with severe respiratory distress in the neonatal period. Disease data Classification Clinical subtype Synonyms CCAM type 3 CCAM typu 3 CPAM typu 3 Wrodzona choroba torbielowata płuc typu 3 Wrodzona torbielowatość gruczolakowata płuc typu 3 CPAM type 3 Congenital cystic adenomatoid malformation of the lung type 3 Congenital cystic adenomatous malformation of the lung type 3 Congenital cystic disease of the lung type 3 ORPHA code 280847 OMIM code - ICD10 code Q33.0 ICD11 code - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl