Primary oculocerebral lymphoma

Orpha code: 279897OMIM code:

Definition

Primary oculocerebral lymphoma is a rare, primary, organ-specific, extranodal non-Hodgkin's lymphoma (typically diffuse large B-cell lymphoma), simultaneously affecting the intraocular compartments (retina, vitreous, optic nerve, uvea and others) and the central nervous system (commonly the cerebellum, spinal cord or pia mater). The presenting symptoms vary depending on the localization of the tumor and may include vitreous floaters or blurred vision, raised intracranial pressure (headache, vomiting, papilledema) and/or focal neurological deficits.

Disease data
Classification

Disease

Synonyms
Primary oculocerebral non-Hodgkin lymphoma
ORPHA code
279897
OMIM code
-
ICD10 code
C85.7
ICD11 code
2B33.5

No additional description.

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