Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition Pachydermoperiostosis (PDP) is a form of primary hypertrophic osteoarthropathy (see this term), a rare hereditary disorder, and is characterized by digital clubbing, pachydermia and subperiosteal new bone formation associated with pain, polyarthritis, <i>cutis verticis gyrata</i>, seborrhea and hyperhidrosis. Three forms have been described: a complete form with pachydermia and periostitis, an incomplete form with evidence of bone abnormalities but lacking pachydermia, and a <i>forme frusta</i> with prominent pachydermia and minimal-to-absent skeletal changes. Disease data Classification Malformation syndrome Synonyms PDP PDP Zespół Touraine'a, Solente i Gole'a Touraine-Solente-Gole syndrome ORPHA code 2796 OMIM code 614441 ICD10 code M89.4 ICD11 code FB86.10 *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl