Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition A form of congenital isolated hyperinsulism characterized by an excessive/ uncontrolled insulin secretion (inappropriate for the level of glycemia), recurrent episodes of profound hypoglycemia and resistance to medical management with diazoxide. Pancreatic involvement can be diffuse or focal. Disease data Classification Clinical group Synonyms Diazoxide-resistant hyperinsulinemic hypoglycemia Hipoglikemia hiperinsulinemiczna oporna na diazoksyd ORPHA code 276585 OMIM code - ICD10 code E16.1 ICD11 code - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl