Description of the disease * EnglishPolish Pobierz sekcję do PDF Definition Pulmonary arterial hypertension associated with portal hypertension (PAH-PH) is a form of pulmonary arterial hypertension (PAH), characterized by an elevated pulmonary arterial resistance leading to right heart failure observed as a complication of portal hypertension. Disease data Classification Clinical group Synonyms PAH associated with portal hypertension Nadciśnienie wrotno-płucne PAH związane z nadciśnieniem wrotnym POPH POPH Portopulmonary hypertension ORPHA code 275813 OMIM code - ICD10 code I27.2 ICD11 code - *Soruce Extended description of the disease Pobierz sekcję do PDF No additional description. Orphanet - interntowa baza danych dotyczących rzadkich chorób i sierochych leków. ©INSERM 1999 - Dostępna na stronie www.orphanet.pl